Infantile fibrosarcoma is a very rare soft tissue tumor that originates most commonly in the body and extremities. We present a neonate with an infantile fibrosarcoma that originated in the ileocecal region and was detected incidentally without symptoms. This is the first case of fibrosarcoma reported in the ileocecal region. Keywords: Colon; Ileocecal; Infantile fibrosarcoma; Neonate; Non-rhabdomyosarcoma.